Hepatic Vein Thrombosis (Budd-Chiari Syndrome)

Budd-Chiari syndrome caused by hepatic vein thrombosis in a patient with myeloproliferative disorder.

We report a 24-year-old Japanese female hospitalized with jaundice and ascites. She exhibited hepatosplenomegaly, severe liver dysfunction, and slight polycythemia with an increase in serum levels of beta-thromboglobin and platelet factor 4. Bone marrow was hypercellular with an increase in progenitor cells. The aggregation response of platelets to ADP and to collagen was markedly increased. Ve...

Infliximab in the treatment of hepatic vein thrombosis (Budd-Chiari syndrome) in three patients with Behcet's syndrome.

Magnetic resonance imaging of the brain showed bilateral hyperintensity of the nucleus dentatus on T2-weighted sequences (Fig. 2). A concurrent brain SPECT demonstrated generalized cortical hypoperfusion. Treatment with chenodeoxycholic acid 750 mg/day was started. One of the most characteristic signs of cerebrotendinous xanthomatosis is the remarkable tendon enlargement due to fat deposition (...

Catheter-directed thrombolytic therapy combined with angioplasty for hepatic vein obstruction in Budd-Chiari syndrome complicated by thrombosis

The aim of this study was to assess the efficacy and safety of catheter-directed thrombolysis combined with angioplasty in the treatment of hepatic vein obstruction in Budd-Chiari syndrome (BCS) complicated by thrombosis. In 14 cases of BCS, the patients with hepatic vein obstruction complicated by thrombosis who underwent catheter-directed urokinase thrombolysis, balloon dilatation and/or sten...

Acute Partial Budd-chiari Syndrome and Portal Vein Thrombosis in Cytomegalovirus Primary Infection

Somatic calreticulin mutations in patients with Budd-Chiari syndrome and portal vein thrombosis.